Abstract
We report a 37-year-old woman with Marfan syndrome (MFS) who presented with acute myelopathy secondary to a subdural spinal hematoma. The patient died of a subarachnoid hemorrhage 4 days later. Autopsy showed a markedly ectatic vertebrobasilar system with fragmentation of the internal elastic lamina. Microscopic examination of the aorta similarly showed a fragmented internal elastic lamina. We discuss the implications of our patient's early onset vertebrobasilar dolichoectasia; this intracranial disease represents a rare cause of subarachnoid hemorrhage in MFS.
Original language | English (US) |
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Pages (from-to) | 196-198 |
Number of pages | 3 |
Journal | Journal of Stroke and Cerebrovascular Diseases |
Volume | 9 |
Issue number | 4 |
DOIs | |
State | Published - Jul 2000 |
Keywords
- Marfan Syndrome
- Myelopathy
- Subarachnoid hemorrage
- Vertobrobasilar dolichoectasia
ASJC Scopus subject areas
- Clinical Neurology
- Surgery
- Health Professions(all)