Ventricular arrhythmias in right ventricular dysplasia/cardiomyopathy

Hugh Calkins, Frank I. Marcus

Research output: Chapter in Book/Report/Conference proceedingChapter

Abstract

Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is a genetic cardiomyopathy characterized by ventricular arrhythmias and structural abnormalities of the right ventricle (RV). In ARVD/C there is progressive replacement of right ventricular myocardium with fatty and fibrous tissue. The precise prevalence of ARVD/C has been estimated to vary between 1 in 1000 and 1 in 5000 of the general population. The purpose of this chapter is to review the current understanding of ARVD/C and its management. Particular attention will be focused on some of the recent advances in the understanding of the genetic basis of ARVD/C and how this information provides insight into the mechanism of ventricular arrhythmias that can cause sudden death.

Original languageEnglish (US)
Title of host publicationElectrical Diseases of the Heart: Genetics, Mechanisms, Treatment, Prevention
PublisherSpringer London
Pages643-653
Number of pages11
ISBN (Print)9781846288531
DOIs
StatePublished - 2008

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Arrhythmogenic Right Ventricular Dysplasia
Cardiomyopathies
Cardiac Arrhythmias
Sudden Death
Heart Ventricles
Adipose Tissue
Cause of Death
Myocardium
Population

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Calkins, H., & Marcus, F. I. (2008). Ventricular arrhythmias in right ventricular dysplasia/cardiomyopathy. In Electrical Diseases of the Heart: Genetics, Mechanisms, Treatment, Prevention (pp. 643-653). Springer London. https://doi.org/10.1007/978-1-84628-854-8_45

Ventricular arrhythmias in right ventricular dysplasia/cardiomyopathy. / Calkins, Hugh; Marcus, Frank I.

Electrical Diseases of the Heart: Genetics, Mechanisms, Treatment, Prevention. Springer London, 2008. p. 643-653.

Research output: Chapter in Book/Report/Conference proceedingChapter

Calkins, H & Marcus, FI 2008, Ventricular arrhythmias in right ventricular dysplasia/cardiomyopathy. in Electrical Diseases of the Heart: Genetics, Mechanisms, Treatment, Prevention. Springer London, pp. 643-653. https://doi.org/10.1007/978-1-84628-854-8_45
Calkins H, Marcus FI. Ventricular arrhythmias in right ventricular dysplasia/cardiomyopathy. In Electrical Diseases of the Heart: Genetics, Mechanisms, Treatment, Prevention. Springer London. 2008. p. 643-653 https://doi.org/10.1007/978-1-84628-854-8_45
Calkins, Hugh ; Marcus, Frank I. / Ventricular arrhythmias in right ventricular dysplasia/cardiomyopathy. Electrical Diseases of the Heart: Genetics, Mechanisms, Treatment, Prevention. Springer London, 2008. pp. 643-653
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