Ventricular arrhythmias in right ventricular dysplasia/cardiomyopathy

Hugh Calkins; Frank I. Marcus

doi:10.1007/978-1-84628-854-8_45

Ventricular arrhythmias in right ventricular dysplasia/cardiomyopathy

Hugh Calkins, Frank I. Marcus

School of Medicine

Research output: Chapter in Book/Report/Conference proceeding › Chapter

Abstract

Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is a genetic cardiomyopathy characterized by ventricular arrhythmias and structural abnormalities of the right ventricle (RV). In ARVD/C there is progressive replacement of right ventricular myocardium with fatty and fibrous tissue. The precise prevalence of ARVD/C has been estimated to vary between 1 in 1000 and 1 in 5000 of the general population. The purpose of this chapter is to review the current understanding of ARVD/C and its management. Particular attention will be focused on some of the recent advances in the understanding of the genetic basis of ARVD/C and how this information provides insight into the mechanism of ventricular arrhythmias that can cause sudden death.

Original language	English (US)
Title of host publication	Electrical Diseases of the Heart
Subtitle of host publication	Genetics, Mechanisms, Treatment, Prevention
Publisher	Springer London
Pages	643-653
Number of pages	11
ISBN (Print)	9781846288531
DOIs	https://doi.org/10.1007/978-1-84628-854-8_45
State	Published - Dec 1 2008

ASJC Scopus subject areas

Medicine(all)

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10.1007/978-1-84628-854-8_45

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abstract = "Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is a genetic cardiomyopathy characterized by ventricular arrhythmias and structural abnormalities of the right ventricle (RV). In ARVD/C there is progressive replacement of right ventricular myocardium with fatty and fibrous tissue. The precise prevalence of ARVD/C has been estimated to vary between 1 in 1000 and 1 in 5000 of the general population. The purpose of this chapter is to review the current understanding of ARVD/C and its management. Particular attention will be focused on some of the recent advances in the understanding of the genetic basis of ARVD/C and how this information provides insight into the mechanism of ventricular arrhythmias that can cause sudden death.",

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AB - Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is a genetic cardiomyopathy characterized by ventricular arrhythmias and structural abnormalities of the right ventricle (RV). In ARVD/C there is progressive replacement of right ventricular myocardium with fatty and fibrous tissue. The precise prevalence of ARVD/C has been estimated to vary between 1 in 1000 and 1 in 5000 of the general population. The purpose of this chapter is to review the current understanding of ARVD/C and its management. Particular attention will be focused on some of the recent advances in the understanding of the genetic basis of ARVD/C and how this information provides insight into the mechanism of ventricular arrhythmias that can cause sudden death.

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Ventricular arrhythmias in right ventricular dysplasia/cardiomyopathy

Abstract

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