Unusual presentation of congenital dermal sinus: Tethered spinal cord with intradural epidermoid and dual paramedian cutaneous ostia

Efrem M. Cox, Kathleen E. Knudson, Sunil Manjila, Alan Cohen

Research output: Contribution to journalArticle

Abstract

The authors present the first report of spinal congenital dermal sinus with paramedian dual ostia leading to 2 intradural epidermoid cysts. This 7-year-old girl had a history of recurrent left paramedian lumbosacral subcutaneous abscesses, with no chemical or pyogenic meningitis. Admission MRI studies demonstrated bilateral lumbar dermal sinus tracts and a tethered spinal cord. At surgery to release the tethered spinal cord the authors encountered paramedian dermal sinus tracts with dual ostia, as well as 2 intradural epidermoid cysts that were not readily apparent on MRI studies. Congenital dermal sinus should be considered in the differential diagnosis of lumbar subcutaneous abscesses, even if the neurocutaneous signatures are located off the midline.

Original languageEnglish (US)
Article numberE5
JournalNeurosurgical Focus
Volume33
Issue number4
DOIs
StatePublished - 2012
Externally publishedYes

Fingerprint

Spina Bifida Occulta
Spinal Cord
Epidermal Cyst
Skin
Abscess
Meningitis
Differential Diagnosis

Keywords

  • Congenital dermal sinus
  • Dual ostia
  • Epidermoid cyst
  • Neural tube defect
  • Tethered spinal cord

ASJC Scopus subject areas

  • Surgery
  • Clinical Neurology

Cite this

Unusual presentation of congenital dermal sinus : Tethered spinal cord with intradural epidermoid and dual paramedian cutaneous ostia. / Cox, Efrem M.; Knudson, Kathleen E.; Manjila, Sunil; Cohen, Alan.

In: Neurosurgical Focus, Vol. 33, No. 4, E5, 2012.

Research output: Contribution to journalArticle

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