Type I chiari malformation: A review of the literature

Jeffery Meadows, Michael Guarnieri, Ken Miller, Raymond Haroun, Michael Kraut, Benjamin S. Carson

Research output: Contribution to journalReview articlepeer-review

17 Scopus citations


More than 100 years after its identification, type I Chiari malformation remains poorly understood. Despite impressive advances in clinical diagnosis, neuroradiology, and neurosurgery, central questions about the pathogenesis, natural history, and prevalence of this condition remain unanswered. Although not common, Chiari malformation should be considered in any patient with signs and symptoms localized to the brain stem or cerebellum, particularly if signs and symptoms coexist with headache and signs of central cord involvement. More importantly, tonsillar ectopia always must be considered in the context of a thorough history and patient evaluation, with recognition that even patients with significant degrees of tonsillar ectopia may remain asymptomatic for extended periods. Craniocervical decompression is the preferred surgical treatment in most cases of type I Chiari malformation with or without syringohydromyelia.

Original languageEnglish (US)
Pages (from-to)220-229
Number of pages10
JournalNeurosurgery Quarterly
Issue number3
StatePublished - Jan 1 2001


  • Arnold-Chiari malformation
  • Chiari malformation
  • Hindbrain herniation
  • Posterior fossa
  • Syringomyelia
  • Syrinx

ASJC Scopus subject areas

  • Surgery
  • Clinical Neurology


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