Thoracic Aortic Aneurysm Syndrome in Children

Giorgio Zanotti; Luca Vricella; Duke Cameron

doi:10.1053/j.pcsu.2008.01.005

Thoracic Aortic Aneurysm Syndrome in Children

Giorgio Zanotti, Luca Vricella, Duke Cameron

School of Medicine

Research output: Contribution to journal › Article › peer-review

30 Scopus citations

Abstract

In contrast with adults, thoracic aortic aneurysms in children are usually associated with connective tissue defect syndromes. As such, there are phenotypic clues to identify patients at risk. Marfan syndrome, Loeys-Dietz syndrome, and bicuspid aortic valve syndrome account for the majority of these aneurysms. Indications for surgery as well as surgical options differ according to diagnosis and are reviewed herein.

Original language	English (US)
Pages (from-to)	11-21
Number of pages	11
Journal	Pediatric Cardiac Surgery Annual
Volume	11
Issue number	1
DOIs	https://doi.org/10.1053/j.pcsu.2008.01.005
State	Published - Apr 9 2008

Keywords

Aneurysm
Loeys-Dietz
Marfan
aorta
bicuspid aortic valve
children

ASJC Scopus subject areas

Pediatrics, Perinatology, and Child Health
Surgery
Cardiology and Cardiovascular Medicine

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10.1053/j.pcsu.2008.01.005

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AU - Cameron, Duke

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KW - aorta

KW - bicuspid aortic valve

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Thoracic Aortic Aneurysm Syndrome in Children

Abstract

Keywords

ASJC Scopus subject areas

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