The usefulness of electroencephalography in Rett syndrome

E. Niedermeyer, S. Naidu, A. Nogueira de Melo

Research output: Contribution to journalArticlepeer-review

Abstract

The Rett syndrome is presumed to be a neurodegenerative disorder of childhood and adolescence occurring solely in girls. The EEG is almost invariably abnormal and frequently demonstrates prominent paroxysmal discharges. This finding corresponds with frequent occurrence of epileptic seizures. Spike activity is quite often accentuated over the central region and may be attenuated or blocked with passive hand movements. Slow spike-waves may also occur. Starting with the end of the first decade, the Rett syndrome tends to lose its progression and comes to a stand-still. Epileptic seizures tend to abate while residual neurological damage (along with EEG slowing) persists. Sleep recordings also show unusual features with decline of physiological patterns and burst-like anterior delta waves.

Original languageEnglish (US)
Pages (from-to)27-37
Number of pages11
JournalAmerican Journal of EEG Technology
Volume31
Issue number1
DOIs
StatePublished - 1991

ASJC Scopus subject areas

  • Neuroscience(all)

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