The Congenital Heart Surgeons' Society Registry of Anomalous Aortic Origin of a Coronary Artery: An update

Julie A. Brothers, J. William Gaynor, Jeffrey P. Jacobs, Jeffrey A. Poynter, Marshall L. Jacobs

Research output: Contribution to journalArticlepeer-review

18 Scopus citations

Abstract

The anomalous aortic origin of a coronary artery from the wrong sinus of Valsalva with an interarterial, intramural, and/or intraconal course is a relatively rare congenital defect of the heart that may be associated with an increased risk of ischaemia of the myocardium and sudden death, notably in children and young adults. Data are limited regarding stratification of risk and long-term outcomes of these patients. In 2009, the Anomalous Coronary Artery Working Group formed the Congenital Heart Surgeons' Society Registry of Anomalous Aortic Origin of a Coronary Artery to obtain information on large numbers of young patients with anomalous aortic origin of a coronary artery with the goal to better understand the natural and surgical history of this anomaly as well as to develop evidence-based treatment and management guidelines. In this report, we describe the data we have collected from the registry and the current state of the registry.

Original languageEnglish (US)
Pages (from-to)1567-1571
Number of pages5
JournalCardiology in the young
Volume25
Issue number8
DOIs
StatePublished - Dec 1 2015

Keywords

  • Congenital cardiac disease
  • interarterial coronary artery
  • intraconal coronary artery
  • intramural coronary artery
  • paediatric cardiac disease

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Cardiology and Cardiovascular Medicine

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