Symptoms and signs in superior canal dehiscence syndrome

Lloyd B. Minor, Phillip D. Cremer, John P Carey, Charles Coleman Della Santina, Sven Olrik Streubel, W. E G Noah

Research output: Contribution to journalArticle

Abstract

Patients with superior canal dehiscence (SCD) syndrome experience vertigo and oscillopsia in response to loud sounds and to stimuli that result in changes in middle ear or intracranial pressure. They may also experience hyperacusis to bone-conducted sounds. The evoked eye movements in this syndrome align with the plane of the dehiscent superior canal. The symptoms and signs can be understood in terms of the effect of the dehiscence in creation of a third mobile window into the inner ear. The SCD syndrome has been diagnosed in 28 patients who were examined in the neuro-otology clinics at the Johns Hopkins Medical Institutions from May 1995 through January 2001. The diagnosis is best established based upon the symptoms that are characteristic for the syndrome, the vertical - torsional eye movements evoked by sound or pressure stimuli noted on examination performed with Frenzel goggles, the lowered thresholds for responses to vestibular-evoked myogenic potentials, and CT imaging of the temporal bones.

Original languageEnglish (US)
Pages (from-to)259-273
Number of pages15
JournalAnnals of the New York Academy of Sciences
Volume942
StatePublished - 2001

Fingerprint

Canals
Signs and Symptoms
Eye movements
Acoustic waves
Bone
Eye Movements
Goggles
Neurotology
Hyperacusis
Vestibular Evoked Myogenic Potentials
Bioelectric potentials
Eye Protective Devices
Temporal Bone
Vertigo
Intracranial Pressure
Middle Ear
Inner Ear
Imaging techniques
Pressure
Bone and Bones

Keywords

  • Nystagmus
  • Oscillopsia
  • Semicircular canal
  • Temporal bone
  • Vertigo
  • Vestibuloocular reflex

ASJC Scopus subject areas

  • Biochemistry, Genetics and Molecular Biology(all)

Cite this

Symptoms and signs in superior canal dehiscence syndrome. / Minor, Lloyd B.; Cremer, Phillip D.; Carey, John P; Della Santina, Charles Coleman; Streubel, Sven Olrik; Noah, W. E G.

In: Annals of the New York Academy of Sciences, Vol. 942, 2001, p. 259-273.

Research output: Contribution to journalArticle

Minor, Lloyd B. ; Cremer, Phillip D. ; Carey, John P ; Della Santina, Charles Coleman ; Streubel, Sven Olrik ; Noah, W. E G. / Symptoms and signs in superior canal dehiscence syndrome. In: Annals of the New York Academy of Sciences. 2001 ; Vol. 942. pp. 259-273.
@article{8ce2180a02094728afed5d271aaec53f,
title = "Symptoms and signs in superior canal dehiscence syndrome",
abstract = "Patients with superior canal dehiscence (SCD) syndrome experience vertigo and oscillopsia in response to loud sounds and to stimuli that result in changes in middle ear or intracranial pressure. They may also experience hyperacusis to bone-conducted sounds. The evoked eye movements in this syndrome align with the plane of the dehiscent superior canal. The symptoms and signs can be understood in terms of the effect of the dehiscence in creation of a third mobile window into the inner ear. The SCD syndrome has been diagnosed in 28 patients who were examined in the neuro-otology clinics at the Johns Hopkins Medical Institutions from May 1995 through January 2001. The diagnosis is best established based upon the symptoms that are characteristic for the syndrome, the vertical - torsional eye movements evoked by sound or pressure stimuli noted on examination performed with Frenzel goggles, the lowered thresholds for responses to vestibular-evoked myogenic potentials, and CT imaging of the temporal bones.",
keywords = "Nystagmus, Oscillopsia, Semicircular canal, Temporal bone, Vertigo, Vestibuloocular reflex",
author = "Minor, {Lloyd B.} and Cremer, {Phillip D.} and Carey, {John P} and {Della Santina}, {Charles Coleman} and Streubel, {Sven Olrik} and Noah, {W. E G}",
year = "2001",
language = "English (US)",
volume = "942",
pages = "259--273",
journal = "Annals of the New York Academy of Sciences",
issn = "0077-8923",
publisher = "Wiley-Blackwell",

}

TY - JOUR

T1 - Symptoms and signs in superior canal dehiscence syndrome

AU - Minor, Lloyd B.

AU - Cremer, Phillip D.

AU - Carey, John P

AU - Della Santina, Charles Coleman

AU - Streubel, Sven Olrik

AU - Noah, W. E G

PY - 2001

Y1 - 2001

N2 - Patients with superior canal dehiscence (SCD) syndrome experience vertigo and oscillopsia in response to loud sounds and to stimuli that result in changes in middle ear or intracranial pressure. They may also experience hyperacusis to bone-conducted sounds. The evoked eye movements in this syndrome align with the plane of the dehiscent superior canal. The symptoms and signs can be understood in terms of the effect of the dehiscence in creation of a third mobile window into the inner ear. The SCD syndrome has been diagnosed in 28 patients who were examined in the neuro-otology clinics at the Johns Hopkins Medical Institutions from May 1995 through January 2001. The diagnosis is best established based upon the symptoms that are characteristic for the syndrome, the vertical - torsional eye movements evoked by sound or pressure stimuli noted on examination performed with Frenzel goggles, the lowered thresholds for responses to vestibular-evoked myogenic potentials, and CT imaging of the temporal bones.

AB - Patients with superior canal dehiscence (SCD) syndrome experience vertigo and oscillopsia in response to loud sounds and to stimuli that result in changes in middle ear or intracranial pressure. They may also experience hyperacusis to bone-conducted sounds. The evoked eye movements in this syndrome align with the plane of the dehiscent superior canal. The symptoms and signs can be understood in terms of the effect of the dehiscence in creation of a third mobile window into the inner ear. The SCD syndrome has been diagnosed in 28 patients who were examined in the neuro-otology clinics at the Johns Hopkins Medical Institutions from May 1995 through January 2001. The diagnosis is best established based upon the symptoms that are characteristic for the syndrome, the vertical - torsional eye movements evoked by sound or pressure stimuli noted on examination performed with Frenzel goggles, the lowered thresholds for responses to vestibular-evoked myogenic potentials, and CT imaging of the temporal bones.

KW - Nystagmus

KW - Oscillopsia

KW - Semicircular canal

KW - Temporal bone

KW - Vertigo

KW - Vestibuloocular reflex

UR - http://www.scopus.com/inward/record.url?scp=0034747882&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=0034747882&partnerID=8YFLogxK

M3 - Article

C2 - 11710468

AN - SCOPUS:0034747882

VL - 942

SP - 259

EP - 273

JO - Annals of the New York Academy of Sciences

JF - Annals of the New York Academy of Sciences

SN - 0077-8923

ER -