Sturge-Weber-syndrom

Frühmanifestation und verlauf in der bilddiagnostik

Translated title of the contribution: Sturge-Weber syndrome: Early manifestation and visualization of disease course

E. Stranzinger, T. A G M Huisman

Research output: Contribution to journalArticle

Abstract

Background. The purpose of this study was to evaluate ultrasound, MRI, and CT investigations in children with Sturge-Weber syndrome. Patients and methods. From 1996 to 2005, a total of 15 investigations of the brain performed in 6 children with Sturge-Weber syndrome were reviewed. We evaluated four ultrasound, five CT, and six MRI exams. Results. With ultrasound an increase of the echogenicity of the periventricular white matter was depicted in the first days of life. MRI is the best modality to demonstrate the vascular malformation, the impaired cerebral venous drainage, and the atrophy of one hemisphere. Conclusions. One-sided periventricular hyperechogenicity on ultrasound can be an early sign of Sturge-Weber syndrome in children with a nevus flammeus. MRI is the method of choice to diagnose Sturge-Weber syndrome and to follow up these children if the neurological status of the patients changes.

Original languageGerman
Pages (from-to)1126-1130
Number of pages5
JournalRadiologe
Volume47
Issue number12
DOIs
StatePublished - Dec 2007
Externally publishedYes

Fingerprint

Sturge-Weber Syndrome
Port-Wine Stain
Vascular Malformations
Atrophy
Drainage
Brain

Keywords

  • Computed tomography (CT)
  • Magnetic resonance imaging (MRI)
  • Sturge-Weber syndrome
  • Ultrasound (US)
  • Vascular malformation

ASJC Scopus subject areas

  • Radiology Nuclear Medicine and imaging
  • Radiological and Ultrasound Technology

Cite this

Sturge-Weber-syndrom : Frühmanifestation und verlauf in der bilddiagnostik. / Stranzinger, E.; Huisman, T. A G M.

In: Radiologe, Vol. 47, No. 12, 12.2007, p. 1126-1130.

Research output: Contribution to journalArticle

Stranzinger, E. ; Huisman, T. A G M. / Sturge-Weber-syndrom : Frühmanifestation und verlauf in der bilddiagnostik. In: Radiologe. 2007 ; Vol. 47, No. 12. pp. 1126-1130.
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