Single-Stage Total Arch Replacement Including Resection of Kommerell Diverticulum in a Patient With Loeys-Dietz Syndrome

Chin Siang Ong, Yuhei Kasai, Souta Fukushima, Narutoshi Hibino, Trent Magruder, Alejandro Suarez-Pierre, Duke Cameron, Luca Vricella

Research output: Contribution to journalArticlepeer-review

Abstract

Loeys-Dietz syndrome (LDS) is an autosomal dominant genetic connective tissue disorder associated with aortic aneurysmal disease. Kommerell diverticulum (KD) is a rare aortic diverticulum, for which the indication for surgery and the surgical techniques remain subjects of debate. We describe our experience with a successful total aortic arch replacement including KD resection through a median sternotomy for a pediatric patient with LDS.

Original languageEnglish (US)
Pages (from-to)651-654
Number of pages4
JournalWorld journal for pediatric & congenital heart surgery
Volume7
Issue number5
DOIs
StatePublished - Sep 1 2016

Keywords

  • Kommerell diverticulum
  • Loeys-Dietz syndrome
  • aberrant right subclavian artery
  • congenital heart disease

ASJC Scopus subject areas

  • Surgery
  • Pediatrics, Perinatology, and Child Health
  • Cardiology and Cardiovascular Medicine

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