Single-Stage Total Arch Replacement Including Resection of Kommerell Diverticulum in a Patient With Loeys-Dietz Syndrome

Chin Siang Ong, Yuhei Kasai, Souta Fukushima, Narutoshi Hibino, Trent Magruder, Alejandro Suarez-Pierre, Duke Cameron, Luca Vricella

Research output: Contribution to journalArticle

Abstract

Loeys-Dietz syndrome (LDS) is an autosomal dominant genetic connective tissue disorder associated with aortic aneurysmal disease. Kommerell diverticulum (KD) is a rare aortic diverticulum, for which the indication for surgery and the surgical techniques remain subjects of debate. We describe our experience with a successful total aortic arch replacement including KD resection through a median sternotomy for a pediatric patient with LDS.

Original languageEnglish (US)
Pages (from-to)651-654
Number of pages4
JournalWorld journal for pediatric & congenital heart surgery
Volume7
Issue number5
DOIs
StatePublished - Sep 1 2016

Fingerprint

Loeys-Dietz Syndrome
Diverticulum
Aortic Diseases
Sternotomy
Thoracic Aorta
Connective Tissue
Pediatrics

Keywords

  • aberrant right subclavian artery
  • congenital heart disease
  • Kommerell diverticulum
  • Loeys-Dietz syndrome

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Surgery
  • Medicine(all)
  • Cardiology and Cardiovascular Medicine

Cite this

Single-Stage Total Arch Replacement Including Resection of Kommerell Diverticulum in a Patient With Loeys-Dietz Syndrome. / Ong, Chin Siang; Kasai, Yuhei; Fukushima, Souta; Hibino, Narutoshi; Magruder, Trent; Suarez-Pierre, Alejandro; Cameron, Duke; Vricella, Luca.

In: World journal for pediatric & congenital heart surgery, Vol. 7, No. 5, 01.09.2016, p. 651-654.

Research output: Contribution to journalArticle

Ong, Chin Siang ; Kasai, Yuhei ; Fukushima, Souta ; Hibino, Narutoshi ; Magruder, Trent ; Suarez-Pierre, Alejandro ; Cameron, Duke ; Vricella, Luca. / Single-Stage Total Arch Replacement Including Resection of Kommerell Diverticulum in a Patient With Loeys-Dietz Syndrome. In: World journal for pediatric & congenital heart surgery. 2016 ; Vol. 7, No. 5. pp. 651-654.
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