Report of the European respiratory society/European cystic fibrosis society task force on the care of adults with cystic fibrosis

J. Stuart Elborn, Scott C. Bell, Susan L. Madge, Pierre Regis Burgel, Carlo Castellani, Steven Conway, Karleen De Rijcke, Birgit Dembski, Pavel Drevinek, Harry G.M. Heijerman, J. Alistair Innes, Anders Lindblad, Bruce Marshall, Hanne V. Olesen, Andreas L. Reimann, Ampara Solé, Laura Viviani, Thomas O.F. Wagner, Tobias Welte, Francesco Blasi

Research output: Contribution to journalArticlepeer-review

Abstract

The improved survival in people with cystic fibrosis has led to an increasing number of patients reaching adulthood. This trend is likely to be maintained over the next decades, suggesting a need to increase the number of centres with expertise in the management of adult patients with cystic fibrosis. These centres should be capable of delivering multidisciplinary care addressing the complexity of the disease, in addition to addressing the psychological burden on patients and their families. Further issues that require attention are organ transplantation and end of life management. Lung disease in adults with cystic fibrosis drives most of the clinical care requirements, and major lifethreatening complications, such as respiratory infection, respiratory failure, pneumothorax and haemoptysis, and the management of lung transplantation require expertise from trained respiratory physicians. The taskforce therefore strongly reccommends that medical leadership in multidisciplinary adult teams should be attributed to a respiratory physician adequately trained in cystic fibrosis management. The task force suggests the implementation of a core curriculum for trainees in adult respiratory medicine and the selection and accreditation of training centres that deliver postgraduate training to the standards of the HERMES programme.

Original languageEnglish (US)
Pages (from-to)420-428
Number of pages9
JournalEuropean Respiratory Journal
Volume47
Issue number2
DOIs
StatePublished - Feb 1 2016
Externally publishedYes

ASJC Scopus subject areas

  • Pulmonary and Respiratory Medicine

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