Rectal bleeding, deep venous thrombosis, and coagulopathy in a patient with Klippel-Trénaunay syndrome

Richard Herman, Shaun Kunisaki, Mark Molitor, Samir Gadepalli, Jonathan R. Dillman, James Geiger

Research output: Contribution to journalArticlepeer-review

Abstract

Klippel-Trénaunay syndrome (KTS) is a rare noninheritable congenital disorder comprising vascular malformations that predispose patients to a paradoxical condition where bleeding occurs in a hypercoagulable state. A 16-year-old boy with a complicated lifetime course of KTS presented with massive rectal bleeding. He underwent a partial colectomy, endorectal resection, and splenectomy. Postoperatively, he developed a saddle pulmonary embolus, ultimately requiring placement of an inferior vena cava filter. He eventually did well and has since had his diverting ostomy reversed and resumed his usual activities. This report validates the use of endorectal resection for venous malformation of the rectum in patients with KTS and highlights the difficult balance of controlling bleeding by correction of a consumptive coagulopathy and the increased risk of thromboembolic complications.

Original languageEnglish (US)
Pages (from-to)598-600
Number of pages3
JournalJournal of pediatric surgery
Volume47
Issue number3
DOIs
StatePublished - Mar 2012
Externally publishedYes

Keywords

  • Coagulopathy
  • DVT
  • Klippel-Trénaunay syndrome
  • Rectal bleeding

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Surgery

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