Puberty in cystic fibrosis

Bracha Goldsweig, Beth Kaminski, Aniket Sidhaye, Scott Blackman, Andrea Kelly

Research output: Contribution to journalArticle

Abstract

Historically, delayed puberty was considered a common clinical feature of cystic fibrosis (CF). More recent reports have documented normal pubertal progression in the majority of individuals with CF. However, youth with more severe disease are still at risk for delayed puberty. Careful evaluation of pubertal development in children and adolescents with CF is important as pubertal timing impacts linear growth, bone mineral accrual, body image and psychosocial wellbeing, all of which can also be impacted directly by CF. This article reviews the physiology of puberty, timing of puberty in CF, evaluation of pubertal development, and the differential diagnosis, evaluation, and management of delayed and precocious puberty in people with CF.

Original languageEnglish (US)
JournalJournal of Cystic Fibrosis
DOIs
StateAccepted/In press - Jan 1 2019

Fingerprint

Puberty
Cystic Fibrosis
Delayed Puberty
Adolescent Development
Precocious Puberty
Body Image
Bone Development
Child Development
Minerals
Differential Diagnosis

Keywords

  • Cystic fibrosis
  • Delayed puberty
  • Growth
  • Puberty

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Pulmonary and Respiratory Medicine

Cite this

Puberty in cystic fibrosis. / Goldsweig, Bracha; Kaminski, Beth; Sidhaye, Aniket; Blackman, Scott; Kelly, Andrea.

In: Journal of Cystic Fibrosis, 01.01.2019.

Research output: Contribution to journalArticle

Goldsweig, Bracha ; Kaminski, Beth ; Sidhaye, Aniket ; Blackman, Scott ; Kelly, Andrea. / Puberty in cystic fibrosis. In: Journal of Cystic Fibrosis. 2019.
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