Persistent primitive hepatic venous plexus with Scimitar syndrome: Description of a case and review of the literature

M. Santiago Restrepo, Osamah Aldoss, Benton Ng

Research output: Contribution to journalArticlepeer-review

Abstract

Persistent primitive hepatic venous plexus is an anomaly of the systemic venous return characterised by postnatal persistence of the foetal intrahepatic venous drainage. Scimitar syndrome is a condition that consists of partial anomalous pulmonary venous return of the right pulmonary venous drainage into the systemic veins, associated with pulmonary artery hypoplasia with the underdeveloped right lung, pulmonary sequestration, and cardiac malposition. Both conditions are rare and together have been rarely described in the literature. We report the first case of this combination of lesions imaged by cardiac magnetic resonance imaging with a three-dimensional reconstruction and reviewed the literature to characterise this uncommon combination.

Original languageEnglish (US)
Pages (from-to)1009-1011
Number of pages3
JournalCardiology in the young
Volume25
Issue number5
DOIs
StatePublished - Jun 10 2015
Externally publishedYes

Keywords

  • partial anomalous pulmonary venous return
  • Persistent primitive hepatic venous plexus
  • Scimitar syndrome

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Cardiology and Cardiovascular Medicine

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