Periampullary neoplasms in von Recklinghausen's disease

Andrew Klein, Jeffrey Clemens, John Cameron

Research output: Contribution to journalReview articlepeer-review

81 Scopus citations


A case of neurofibromatosis is reported in a patient who was initially seen with obstructive jaundice caused by a carcinoid tumor originating from the ampulla of Vater. An extensive review of the literature suggests that patients with von Recklinghausen's disease are at significant risk for periampullary neoplasms of neural-crest and non-neural-crest origin. The tendency of those tumors to arise from the ampulla of Vater has diagnostic and therapeutic implications.

Original languageEnglish (US)
Pages (from-to)815-819
Number of pages5
Issue number5
StatePublished - Nov 1989

ASJC Scopus subject areas

  • Surgery


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