Pentalogy of cantrell with ectopia cordis: CT findings

Ali Pirasteh, Carolina Carcano, Jacobo Kirsch, Tan Lucien H. Mohammed

Research output: Contribution to journalArticlepeer-review

Abstract

A 14-month-old girl with pentalogy of Cantrell, a very rare congenital syndrome characterized by an epigastric omphalocele and malformations of the heart, sternum, pericardium, and diaphragm, underwent echocardiography and multidetector computed tomography before surgical repair of these deformities was attempted. These tests revealed multiple cardiovascular and noncardiovascular abnormalities. After surgery, the patient's cardiovascular status was stable. Although studies have shown that echocardiography, multidetector computed tomography, and magnetic resonance imaging may each play a role in the diagnosis and management of this condition, there are few data available to support the use of one imaging modality over another.

Original languageEnglish (US)
Pages (from-to)29-34
Number of pages6
JournalJournal of Radiology Case Reports
Volume8
Issue number12
DOIs
StatePublished - Jan 1 2014

Keywords

  • Cardiac malformation
  • Ectopia Cordis
  • MDCT
  • Omphalocele
  • Pentalogy of cantrell

ASJC Scopus subject areas

  • Radiology Nuclear Medicine and imaging

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