TY - JOUR
T1 - Pentalogy of cantrell with ectopia cordis
T2 - CT findings
AU - Pirasteh, Ali
AU - Carcano, Carolina
AU - Kirsch, Jacobo
AU - Mohammed, Tan Lucien H.
N1 - Publisher Copyright:
© 2014, EduRad. All rights reserved.
PY - 2014
Y1 - 2014
N2 - A 14-month-old girl with pentalogy of Cantrell, a very rare congenital syndrome characterized by an epigastric omphalocele and malformations of the heart, sternum, pericardium, and diaphragm, underwent echocardiography and multidetector computed tomography before surgical repair of these deformities was attempted. These tests revealed multiple cardiovascular and noncardiovascular abnormalities. After surgery, the patient's cardiovascular status was stable. Although studies have shown that echocardiography, multidetector computed tomography, and magnetic resonance imaging may each play a role in the diagnosis and management of this condition, there are few data available to support the use of one imaging modality over another.
AB - A 14-month-old girl with pentalogy of Cantrell, a very rare congenital syndrome characterized by an epigastric omphalocele and malformations of the heart, sternum, pericardium, and diaphragm, underwent echocardiography and multidetector computed tomography before surgical repair of these deformities was attempted. These tests revealed multiple cardiovascular and noncardiovascular abnormalities. After surgery, the patient's cardiovascular status was stable. Although studies have shown that echocardiography, multidetector computed tomography, and magnetic resonance imaging may each play a role in the diagnosis and management of this condition, there are few data available to support the use of one imaging modality over another.
KW - Cardiac malformation
KW - Ectopia Cordis
KW - MDCT
KW - Omphalocele
KW - Pentalogy of cantrell
UR - http://www.scopus.com/inward/record.url?scp=84919668606&partnerID=8YFLogxK
UR - http://www.scopus.com/inward/citedby.url?scp=84919668606&partnerID=8YFLogxK
U2 - 10.3941/jrcr.v8i12.1972
DO - 10.3941/jrcr.v8i12.1972
M3 - Article
C2 - 25926914
AN - SCOPUS:84919668606
SN - 1943-0922
VL - 8
SP - 29
EP - 34
JO - Journal of Radiology Case Reports
JF - Journal of Radiology Case Reports
IS - 12
ER -