Ocular motor dysfunction in Parry-Romberg syndrome

four cases.

Christina Rapp Prescott, M. Joshua Hasbani, Andrew J. Levada, Jonathan E. Silbert, Jacqueline M S Winterkorn, Robert L. Lesser

Research output: Contribution to journalArticle

Abstract

The authors describe four patients with Parry-Romberg syndrome (PRS) who had abnormal eye movements, ptosis, and facial hemiatrophy. There were delays in diagnosis in all cases, often requiring multiple imaging studies, prior to diagnosis of PRS. These cases demonstrate the variable ophthalmic manifestations of PRS, which can lead to difficulty in diagnosis. Case 1 was a 23-year-old woman with lateral rectus paresis who presented with horizontal diplopia and developed ptosis and facial hemiatrophy. Case 2 was a 28-year-old woman with medial rectus weakness adjusted to diplopia by head turn and gaze preference. Case 3 was a 68-year-old woman who presented with dry eye symptoms and was noted to prefer right gaze and have left hemifacial atrophy. Case 4 was a 68-year-old woman who presented with ptosis, enophthalmos, and restriction of up gaze. The ocular motor defect in all of these cases is best explained by muscle fibrosis rather than nerve paresis.

Original languageEnglish (US)
JournalJournal of Pediatric Ophthalmology and Strabismus
Volume48 Online
StatePublished - 2011
Externally publishedYes

Fingerprint

Facial Hemiatrophy
Diplopia
Paresis
Eye Manifestations
Enophthalmos
Dyskinesias
Eye Movements
Fibrosis
Head
Muscles

ASJC Scopus subject areas

  • Ophthalmology
  • Pediatrics, Perinatology, and Child Health

Cite this

Prescott, C. R., Hasbani, M. J., Levada, A. J., Silbert, J. E., Winterkorn, J. M. S., & Lesser, R. L. (2011). Ocular motor dysfunction in Parry-Romberg syndrome: four cases. Journal of Pediatric Ophthalmology and Strabismus, 48 Online.

Ocular motor dysfunction in Parry-Romberg syndrome : four cases. / Prescott, Christina Rapp; Hasbani, M. Joshua; Levada, Andrew J.; Silbert, Jonathan E.; Winterkorn, Jacqueline M S; Lesser, Robert L.

In: Journal of Pediatric Ophthalmology and Strabismus, Vol. 48 Online, 2011.

Research output: Contribution to journalArticle

Prescott, CR, Hasbani, MJ, Levada, AJ, Silbert, JE, Winterkorn, JMS & Lesser, RL 2011, 'Ocular motor dysfunction in Parry-Romberg syndrome: four cases.', Journal of Pediatric Ophthalmology and Strabismus, vol. 48 Online.
Prescott CR, Hasbani MJ, Levada AJ, Silbert JE, Winterkorn JMS, Lesser RL. Ocular motor dysfunction in Parry-Romberg syndrome: four cases. Journal of Pediatric Ophthalmology and Strabismus. 2011;48 Online.
Prescott, Christina Rapp ; Hasbani, M. Joshua ; Levada, Andrew J. ; Silbert, Jonathan E. ; Winterkorn, Jacqueline M S ; Lesser, Robert L. / Ocular motor dysfunction in Parry-Romberg syndrome : four cases. In: Journal of Pediatric Ophthalmology and Strabismus. 2011 ; Vol. 48 Online.
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