Abstract
Otocephaly is a craniofacial syndrome with a constellation of findings consistent with symmetrically deficient development of the first branchial arch. Characteristically, those affected have ventrally displaced ears, microstomia, and an atrophic to absent mandible. Secondary to oropharyngeal incompetence, ventilatory difficulties typically lead to the imminent death of these infants shortly after birth. Here we present a patient who survived well beyond the perinatal period with the support of pediatric intensivists and advanced technology available for the diagnosis and treatment of such a complex craniofacial syndrome.
Original language | English (US) |
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Pages (from-to) | 372-375 |
Number of pages | 4 |
Journal | Journal of Craniofacial Surgery |
Volume | 7 |
Issue number | 5 |
DOIs | |
State | Published - Sep 1996 |
Externally published | Yes |
Keywords
- Oropharyngeal incompetence
- Otocephaly
ASJC Scopus subject areas
- Surgery
- Otorhinolaryngology