Morquio's syndrome and its anaesthetic considerations

Kathleen A. Morgan, Mohamed Rehman, Roy E. Schwartz

Research output: Contribution to journalArticle

Abstract

Morquio's syndrome is an inherited disorder characterized by excessive excretion of keratan sulphate in the urine. The anaesthetic care of these patients should take into consideration respiratory, craniofacial, cardiac, skeletal, ocular and hepatic abnormalities. We report the case of a child with Morquio's syndrome who presented for stabilization of the cervical spine, and discuss the issues relevant to the anaesthesiologist.

Original languageEnglish (US)
Pages (from-to)641-644
Number of pages4
JournalPaediatric Anaesthesia
Volume12
Issue number7
DOIs
StatePublished - Nov 14 2002
Externally publishedYes

Fingerprint

Mucopolysaccharidosis IV
Anesthetics
Eye Abnormalities
Keratan Sulfate
Patient Care
Spine
Urine
Liver

Keywords

  • Dwarfism
  • Morquio's syndrome
  • Mucopolysaccharidosis
  • Unstable neck

ASJC Scopus subject areas

  • Anesthesiology and Pain Medicine
  • Pediatrics, Perinatology, and Child Health

Cite this

Morquio's syndrome and its anaesthetic considerations. / Morgan, Kathleen A.; Rehman, Mohamed; Schwartz, Roy E.

In: Paediatric Anaesthesia, Vol. 12, No. 7, 14.11.2002, p. 641-644.

Research output: Contribution to journalArticle

Morgan, Kathleen A. ; Rehman, Mohamed ; Schwartz, Roy E. / Morquio's syndrome and its anaesthetic considerations. In: Paediatric Anaesthesia. 2002 ; Vol. 12, No. 7. pp. 641-644.
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