Mirizzi syndrome secondary to an adenoma of the cystic duct

Shaun M. Kunisaki, Martin Hertl, Bruce E. Bodner, A. Benedict Cosimi

Research output: Contribution to journalArticle

Abstract

Bile duct adenomas are uncommon lesions that can cause obstructive jaundice. We report the unusual case of a 54-year-old man who developed Mirizzi syndrome secondary to a bile duct papillary adenoma located in the cystic duct remnant. A case report is presented, together with a review of extrahepatic bile duct adenomas published in the English-language literature, with special attention directed toward the clinical manifestations, locations, and prognosis of these tumors. Bile duct adenomas are very rare tumors. Although cholangiography can detect many of these lesions, few cases were correctly diagnosed preoperatively. Most lesions were located in the distal common bile duct or at the ampulla of Vater. Pathologic examination often revealed foci of carcinoma in situ, dysplasia, or atypia. Local resection was performed in most cases. There were no previous case reports of extrinsic common bile duct obstruction caused by tumors within the cystic duct. We describe here a very rare, acalculous variant of Mirizzi syndrome secondary to a solitary papillary adenoma of the cystic duct. In general, bile duct adenomas are uncommon lesions that are difficult to diagnoses preoperatively. These tumors usually present with jaundice secondary to intraluminal biliary obstruction. These lesions are premalignant and should be managed by complete surgical resection.

Original languageEnglish (US)
Pages (from-to)159-162
Number of pages4
JournalJournal of Hepato-Biliary-Pancreatic Surgery
Volume12
Issue number2
DOIs
StatePublished - Apr 1 2005

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Keywords

  • Bileduct adenoma
  • Cystic duct
  • Mirizzi syndrome

ASJC Scopus subject areas

  • Surgery
  • Hepatology

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