Linear morphea of the forehead (en coup de sabre)

Kristen Miller, Stephanie Lehrhoff, Max Fischer, Shane Meehan, Jo Ann Latkowski

Research output: Contribution to journalArticle

Abstract

Linear morphea of the forehead or en coup de sabre (ECDS) is an unusual variant of morphea. It typically occurs in children although cases of adult-onset ECDS exist as reported here. ECDS has a specific distribution on the frontal scalp and forehead and is usually unilateral. Sclerosis in ECDS lesions may invade deeply to involve underlying muscle and bone and may exist on the same clinicopathologic spectrum as Parry-Romberg syndrome. Extracutaneous involvement is frequent, with neurologic and ophthalmologic findings occurring most commonly. The etiology of ECDS is unclear but may be autoimmune in origin. The question of whether Borrelia infection also plays a role remains controversial. Current evidence supports first-line treatment with methotrexate and oral glucocorticoids followed by phototherapy and mycophenolate mofetil.

Original languageEnglish (US)
Pages (from-to)22
Number of pages1
JournalDermatology Online Journal
Volume18
Issue number12
StatePublished - Dec 2012
Externally publishedYes

Fingerprint

Localized Scleroderma
Forehead
Facial Hemiatrophy
Borrelia Infections
Mycophenolic Acid
Phototherapy
Sclerosis
Neurologic Manifestations
Scalp
Methotrexate
Glucocorticoids
Bone and Bones
Muscles
Therapeutics

ASJC Scopus subject areas

  • Dermatology

Cite this

Miller, K., Lehrhoff, S., Fischer, M., Meehan, S., & Latkowski, J. A. (2012). Linear morphea of the forehead (en coup de sabre). Dermatology Online Journal, 18(12), 22.

Linear morphea of the forehead (en coup de sabre). / Miller, Kristen; Lehrhoff, Stephanie; Fischer, Max; Meehan, Shane; Latkowski, Jo Ann.

In: Dermatology Online Journal, Vol. 18, No. 12, 12.2012, p. 22.

Research output: Contribution to journalArticle

Miller, K, Lehrhoff, S, Fischer, M, Meehan, S & Latkowski, JA 2012, 'Linear morphea of the forehead (en coup de sabre)', Dermatology Online Journal, vol. 18, no. 12, pp. 22.
Miller K, Lehrhoff S, Fischer M, Meehan S, Latkowski JA. Linear morphea of the forehead (en coup de sabre). Dermatology Online Journal. 2012 Dec;18(12):22.
Miller, Kristen ; Lehrhoff, Stephanie ; Fischer, Max ; Meehan, Shane ; Latkowski, Jo Ann. / Linear morphea of the forehead (en coup de sabre). In: Dermatology Online Journal. 2012 ; Vol. 18, No. 12. pp. 22.
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