Isolated pediatric hemihyperplasia requiring surgical debulking of the thigh

Benjamin D. Schultz; Devin Coon; Miguel Medina; Julie Hoover-Fong; Paul D. Sponseller; Amir H. Dorafshar

doi:10.1016/j.epsc.2014.12.005

Isolated pediatric hemihyperplasia requiring surgical debulking of the thigh

Benjamin D. Schultz, Devin Coon, Miguel Medina, Julie Hoover-Fong, Paul D. Sponseller, Amir H. Dorafshar

School of Medicine

Research output: Contribution to journal › Article › peer-review

Abstract

Isolated Hemihyperplasia (IHH) is a rare disorder that results in the enlargement of a portion of a limb, a complete limb or an entire half of an individual's body. We describe an 11 year-old girl with isolated hemihyperplasia of her right upper and lower extremities, breast, and vulvar region. A mass consisting of asymmetric enlargement and fatty infiltration of the right adductor compartment was first noticed at approximately 4 years of life and progressed dramatically to severely affect her gait. We surgically debulked the thigh and resected the excess skin to restore symmetry. The patient did well postoperatively, achieved excellent cosmesis, and restoration of gait.

Original language	English (US)
Pages (from-to)	53-57
Number of pages	5
Journal	Journal of Pediatric Surgery Case Reports
Volume	3
Issue number	2
DOIs	https://doi.org/10.1016/j.epsc.2014.12.005
State	Published - Feb 2015

Keywords

Hemihyperplasia
Hemihypertrophy
Overgrowth syndrome
Pediatrics
Surgery

ASJC Scopus subject areas

Pediatrics, Perinatology, and Child Health
Surgery

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10.1016/j.epsc.2014.12.005

Cite this

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title = "Isolated pediatric hemihyperplasia requiring surgical debulking of the thigh",

abstract = "Isolated Hemihyperplasia (IHH) is a rare disorder that results in the enlargement of a portion of a limb, a complete limb or an entire half of an individual's body. We describe an 11 year-old girl with isolated hemihyperplasia of her right upper and lower extremities, breast, and vulvar region. A mass consisting of asymmetric enlargement and fatty infiltration of the right adductor compartment was first noticed at approximately 4 years of life and progressed dramatically to severely affect her gait. We surgically debulked the thigh and resected the excess skin to restore symmetry. The patient did well postoperatively, achieved excellent cosmesis, and restoration of gait.",

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AU - Coon, Devin

AU - Medina, Miguel

AU - Hoover-Fong, Julie

AU - Sponseller, Paul D.

AU - Dorafshar, Amir H.

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AB - Isolated Hemihyperplasia (IHH) is a rare disorder that results in the enlargement of a portion of a limb, a complete limb or an entire half of an individual's body. We describe an 11 year-old girl with isolated hemihyperplasia of her right upper and lower extremities, breast, and vulvar region. A mass consisting of asymmetric enlargement and fatty infiltration of the right adductor compartment was first noticed at approximately 4 years of life and progressed dramatically to severely affect her gait. We surgically debulked the thigh and resected the excess skin to restore symmetry. The patient did well postoperatively, achieved excellent cosmesis, and restoration of gait.

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Isolated pediatric hemihyperplasia requiring surgical debulking of the thigh

Abstract

Keywords

ASJC Scopus subject areas

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