Aneurysm of the ascending aorta due to cystic medial necrosis is usually the first aortic manifestation of Marfan's syndrome. Aneurysm of the descending thoracic aorta in the patient with Marfan's syndrome has been associated with ascending aortic and, often, abdominal aneurysmal disease.1,2 We recently treated a woman with features characteristic of Marfan's syndrome who had an isolated aneurysm of the descending thoracic aorta. To our knowledge, only 1 other such case has been reported previously.3.
ASJC Scopus subject areas
- Cardiology and Cardiovascular Medicine