We report a case of life-threatening hematemesis due to portal hypertension caused by an isolated arterio-portal fistula (APF). Intrahepatic APFs are extremely rare and are a cause of presinusoidal portal hypertension. Etiologies for APFs are comprised of precipitating trauma, malignancy, and hereditary hemorrhagic telan-giectasia, but these were not the case in our patient. Idiopathic APFs are usually due to congenital vascular abnormalities and thus usually present in the pediatric setting. This is one of the first cases of adult-onset isolated APF who presented with portal hypertension and was successfully managed through endoscopic hemostasis and subsequent interventional radiological embolization.
- Arterioportal fistula
- Hepatic artery embolization
- Hepatic vein pressure gradient
- Pre-sinusoidal portal hypertension
ASJC Scopus subject areas