Intrathoracic pleomorphic liposarcoma in a child: Study of an unusual case

Syed Z Ali, Saul Teichberg, Ellen Kahn, Steven I. Hajdu

Research output: Contribution to journalArticle

Abstract

Primary intrathoracic liposarcoma is an extremely rare neoplasm in the pediatric age group. We report an unusual case of a 3-year-old boy who presented with a large intrathoracic tumor arising from the right chest wall. Biopsy showed a pleomorphic sarcoma with histological, immunohistochemical, and ultrastructural features of pleomorphic liposarcoma. The tumor displayed an aggressive clinical behavior, and the patient continued to have recurrences despite rigorous chemotherapy and radiation treatment. He subsequently died 2 years after the initial diagnosis.

Original languageEnglish (US)
Pages (from-to)99-105
Number of pages7
JournalFetal and Pediatric Pathology
Volume16
Issue number1
DOIs
StatePublished - 1996

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Liposarcoma
Neoplasms
Thoracic Wall
Sarcoma
Age Groups
Radiation
Pediatrics
Biopsy
Recurrence
Drug Therapy
Therapeutics

Keywords

  • chest wall
  • childhood
  • intrathoracic
  • Liposarcoma

ASJC Scopus subject areas

  • Pathology and Forensic Medicine
  • Pediatrics, Perinatology, and Child Health

Cite this

Intrathoracic pleomorphic liposarcoma in a child : Study of an unusual case. / Ali, Syed Z; Teichberg, Saul; Kahn, Ellen; Hajdu, Steven I.

In: Fetal and Pediatric Pathology, Vol. 16, No. 1, 1996, p. 99-105.

Research output: Contribution to journalArticle

Ali, Syed Z ; Teichberg, Saul ; Kahn, Ellen ; Hajdu, Steven I. / Intrathoracic pleomorphic liposarcoma in a child : Study of an unusual case. In: Fetal and Pediatric Pathology. 1996 ; Vol. 16, No. 1. pp. 99-105.
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