Incontinentia pigmenti

Research output: Contribution to journalReview article


IP is a distinct neurocutaneous syndrome with a high incidence of systemic findings. It should be suspected in patients who present with characteristic cutaneous stigmata. However, skin markers may be subtle in older children and adults. Evaluation of patients with IP requires a meticulous search for cutaneous and extracutaneous manifestations of the syndrome. Management should focus on genetic counseling and potentially serious complications involving the eyes, teeth, nad CNS.

Original languageEnglish (US)
Pages (from-to)361-377
Number of pages17
JournalNeurologic clinics
Issue number3
StatePublished - Dec 1 1987


ASJC Scopus subject areas

  • Clinical Neurology

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