Hypoplastic left heart syndrome: From fetus to fontan

Peter P. Roeleveld, David M. Axelrod, Darren Klugman, Melissa B. Jones, Nikhil K. Chanani, Joseph W. Rossano, John M. Costello

Research output: Contribution to journalArticlepeer-review

Abstract

The care of children with hypoplastic left heart syndrome is constantly evolving. Prenatal diagnosis of hypoplastic left heart syndrome will aid in counselling of parents, and selected fetuses may be candidates for in utero intervention. Following birth, palliation can be undertaken through staged operations: Norwood (or hybrid) in the 1st week of life, superior cavopulmonary connection at 4-6 months of life, and finally total cavopulmonary connection (Fontan) at 2-4 years of age. Children with hypoplastic left heart syndrome are at risk of circulatory failure their entire life, and selected patients may undergo heart transplantation. In this review article, we summarise recent advances in the critical care management of patients with hypoplastic left heart syndrome as were discussed in a focused session at the 12th International Conference of the Paediatric Cardiac Intensive Care Society held on 9 December, 2016, in Miami Beach, Florida.

Original languageEnglish (US)
Pages (from-to)1275-1288
Number of pages14
JournalCardiology in the young
Volume28
Issue number11
DOIs
StatePublished - Nov 1 2018
Externally publishedYes

Keywords

  • critical care management
  • Hypoplastic left heart syndrome
  • review

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Cardiology and Cardiovascular Medicine

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