Human C9ORF72 Hexanucleotide Expansion Reproduces RNA Foci and Dipeptide Repeat Proteins but Not Neurodegeneration in BAC Transgenic Mice

Owen M. Peters, Gabriela Toro Cabrera, Helene Tran, Tania F. Gendron, Jeanne E. McKeon, Jake Metterville, Alexandra Weiss, Nicholas Wightman, Johnny Salameh, Juhyun Kim, Huaming Sun, Kevin B. Boylan, Dennis Dickson, Zachary Kennedy, Ziqiang Lin, Yong Jie Zhang, Lillian Daughrity, Chris Jung, Fen Biao Gao, Peter C. SappH. Robert Horvitz, Daryl A. Bosco, Solange P. Brown, Pieter de Jong, Leonard Petrucelli, Christian Mueller, Robert H. Brown

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