Fourth ventricular hemangioblastoma associated with pheochromocytoma and renal medullary fibroma

Susan J. Ehrenpreis, Donald A. Kristt, Daniele Rigamonti

Research output: Contribution to journalArticlepeer-review

Abstract

Intraventricular hemangioblastomas are exceptionally rare. Of the cases described in the literature, very few were associated with von Hippel-Lindau disease. We present a highly unusual case of a fourth ventricular hemangioblastoma associated with a pheochromocytoma and a renal medullary fibroma. This may represent a forme fruste of the von Hippel-Lindau complex. A workup for papilledema resulted in the discovery of this rare finding.

Original languageEnglish (US)
Pages (from-to)183-187
Number of pages5
JournalJournal of Neuro-Ophthalmology
Volume14
Issue number3
DOIs
StatePublished - Sep 1994

Keywords

  • Hemangioblastoma
  • Pheochromocytoma
  • Renal medullary fibroma

ASJC Scopus subject areas

  • Ophthalmology
  • Clinical Neurology

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