Familial congenital bicuspid aortic valve. Secondary calcific aortic stenosis and aortic aneurysm

A. N. Gale, V. A. McKusick, G. M. Hutchins, Vincent L Gott

Research output: Contribution to journalArticle

Abstract

A patient with an aneurysm of the ascending aorta and calcific stenosis of a congenital bicuspid aortic valve, whose brother also had a stenotic congenital bicuspid aortic valve, is described. Predominant aortic stenosis at cardiac catheterization and the presence of an aneurysm distal to and not including the aortic valvular ring made the initial diagnosis of Marfan's syndrome unlikely. Cystic medial necrosis present in the aneurysmal wall probably arose as a consequence of poststenotic dilatation. Adequate noninvasive evaluation of the ascending aorta requires echocardiographic studies, as well as a chest X-ray film.

Original languageEnglish (US)
Pages (from-to)668-670
Number of pages3
JournalChest
Volume72
Issue number5
StatePublished - 1977

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Aortic Aneurysm
Aneurysm
Aorta
Marfan Syndrome
X-Ray Film
Aortic Valve Stenosis
Cardiac Catheterization
Siblings
Dilatation
Pathologic Constriction
Necrosis
Thorax
Bicuspid Aortic Valve
Calcification of Aortic Valve

ASJC Scopus subject areas

  • Pulmonary and Respiratory Medicine

Cite this

Familial congenital bicuspid aortic valve. Secondary calcific aortic stenosis and aortic aneurysm. / Gale, A. N.; McKusick, V. A.; Hutchins, G. M.; Gott, Vincent L.

In: Chest, Vol. 72, No. 5, 1977, p. 668-670.

Research output: Contribution to journalArticle

Gale, AN, McKusick, VA, Hutchins, GM & Gott, VL 1977, 'Familial congenital bicuspid aortic valve. Secondary calcific aortic stenosis and aortic aneurysm', Chest, vol. 72, no. 5, pp. 668-670.
Gale, A. N. ; McKusick, V. A. ; Hutchins, G. M. ; Gott, Vincent L. / Familial congenital bicuspid aortic valve. Secondary calcific aortic stenosis and aortic aneurysm. In: Chest. 1977 ; Vol. 72, No. 5. pp. 668-670.
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