Epithelioid Angiomyolipoma in a Pediatric Patient: Case Report and Review of Literature

Michael H. Johnson, Joseph B. Song, Louis P. Dehner, Robert Sherburne Figenshau

Research output: Contribution to journalArticlepeer-review


We report a case of a 17-year-old girl with tuberous sclerosis complex who underwent partial nephrectomy for a newly discovered 7.5-cm renal mass subsequently determined to be an epithelioid angiomyolipoma, a rare variant of angiomyolipoma that can be confused clinically, radiographically, and pathologically for renal cell carcinoma. Proper diagnosis and treatment are critical, especially in the pediatric patient. This case report and review of literature serve at increasing the awareness of this renal tumor, with its somewhat unpredictable outcome, reviewing the pertinent literature on the topic of epithelioid angiomyolipoma in the clinical setting of tuberous sclerosis complex.

Original languageEnglish (US)
Pages (from-to)159-161
Number of pages3
JournalUrology Case Reports
Issue number5
StatePublished - Sep 2014


  • Angiomyolipoma
  • Epithelioid angiomyolipoma
  • Kidney
  • Tuberous sclerosis complex

ASJC Scopus subject areas

  • Urology


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