Disproportionately severe calcinosis cutis in an 88-year-old patient with CREST syndrome

J. M. Buchowski, Nicholas U. Ahn, U. M. Ahn, Edward F McCarthy, M. B. Mehta

Research output: Contribution to journalArticle

Abstract

An 88-year-old woman with CREST syndrome (calcinosis, Raynaud's phenomenon, esophageal dysmotility, sclerodactyly, and telangiectasias) presented with hyperglycemia, intravascular depletion, and atrial fibrillation. The patient was found to have unusually severe calcinosis cutis in both legs extending from the knees to the ankles bilaterally, as well as Raynaud's phenomenon, sclerodactyly, and telangiectasias. The patient was normocalcemic and normophosphatemic. Although subcutaneous calcification is often seen with CREST syndrome, this case is unusual in that the area of involvement was much larger than previously described. Furthermore, the amount of calcinosis was disproportionately severe and was the major cause of symptoms and disability compared with the other components of the syndrome.

Original languageEnglish (US)
Pages (from-to)478-481
Number of pages4
JournalSkeletal Radiology
Volume30
Issue number8
DOIs
StatePublished - 2001

Fingerprint

CREST Syndrome
Calcinosis
Telangiectasis
Raynaud Disease
Esophageal Motility Disorders
Ankle
Hyperglycemia
Atrial Fibrillation
Leg
Knee

Keywords

  • Calcification
  • CREST syndrome
  • Dystrophic calcinosis cutis
  • Lower extremities
  • Radiographs

ASJC Scopus subject areas

  • Radiology Nuclear Medicine and imaging
  • Radiological and Ultrasound Technology

Cite this

Disproportionately severe calcinosis cutis in an 88-year-old patient with CREST syndrome. / Buchowski, J. M.; Ahn, Nicholas U.; Ahn, U. M.; McCarthy, Edward F; Mehta, M. B.

In: Skeletal Radiology, Vol. 30, No. 8, 2001, p. 478-481.

Research output: Contribution to journalArticle

Buchowski, J. M. ; Ahn, Nicholas U. ; Ahn, U. M. ; McCarthy, Edward F ; Mehta, M. B. / Disproportionately severe calcinosis cutis in an 88-year-old patient with CREST syndrome. In: Skeletal Radiology. 2001 ; Vol. 30, No. 8. pp. 478-481.
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