Diffuse esophageal leiomyomatosis in a patient with Alport syndrome: CT demonstration

Lindsey S. Rabushka; Elliot K. Fishman; Janet E. Kuhlman; Ralph H. Hruban

doi:10.1148/radiology.179.1.2006273

Diffuse esophageal leiomyomatosis in a patient with Alport syndrome: CT demonstration

Lindsey S. Rabushka, Elliot K. Fishman, Janet E. Kuhlman, Ralph H. Hruban

School of Medicine

Research output: Contribution to journal › Article › peer-review

43 Scopus citations

Abstract

In a patient with progressive dysphagia, postprandial vomiting, and a history of Alport syndrome, barium and manometric studies had been interpreted as consistent with achalasia, but a subsequent computed tomographic (CT) scan of the thorax was suggestive of a lower esophageal intramural mass. Multiple leiomyomas of the esophagus were later proved at thoracotomy. Differences between adult and pediatric leiomyomas and the association of leiomyomas with Alport syndrome are discussed.

Original language	English (US)
Pages (from-to)	176-178
Number of pages	3
Journal	RADIOLOGY
Volume	179
Issue number	1
DOIs	https://doi.org/10.1148/radiology.179.1.2006273
State	Published - Apr 1991

Keywords

Alport syndrome
Children, gastrointestinal tract
Esophagus, CT, 71.1211
Esophagus, neoplasms, 71.3131
Myoma, 71.3131

ASJC Scopus subject areas

Radiology Nuclear Medicine and imaging

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10.1148/radiology.179.1.2006273

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title = "Diffuse esophageal leiomyomatosis in a patient with Alport syndrome: CT demonstration",

abstract = "In a patient with progressive dysphagia, postprandial vomiting, and a history of Alport syndrome, barium and manometric studies had been interpreted as consistent with achalasia, but a subsequent computed tomographic (CT) scan of the thorax was suggestive of a lower esophageal intramural mass. Multiple leiomyomas of the esophagus were later proved at thoracotomy. Differences between adult and pediatric leiomyomas and the association of leiomyomas with Alport syndrome are discussed.",

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author = "Rabushka, {Lindsey S.} and Fishman, {Elliot K.} and Kuhlman, {Janet E.} and Hruban, {Ralph H.}",

year = "1991",

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T1 - Diffuse esophageal leiomyomatosis in a patient with Alport syndrome

T2 - CT demonstration

AU - Rabushka, Lindsey S.

AU - Fishman, Elliot K.

AU - Kuhlman, Janet E.

AU - Hruban, Ralph H.

PY - 1991/4

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N2 - In a patient with progressive dysphagia, postprandial vomiting, and a history of Alport syndrome, barium and manometric studies had been interpreted as consistent with achalasia, but a subsequent computed tomographic (CT) scan of the thorax was suggestive of a lower esophageal intramural mass. Multiple leiomyomas of the esophagus were later proved at thoracotomy. Differences between adult and pediatric leiomyomas and the association of leiomyomas with Alport syndrome are discussed.

AB - In a patient with progressive dysphagia, postprandial vomiting, and a history of Alport syndrome, barium and manometric studies had been interpreted as consistent with achalasia, but a subsequent computed tomographic (CT) scan of the thorax was suggestive of a lower esophageal intramural mass. Multiple leiomyomas of the esophagus were later proved at thoracotomy. Differences between adult and pediatric leiomyomas and the association of leiomyomas with Alport syndrome are discussed.

KW - Alport syndrome

KW - Children, gastrointestinal tract

KW - Esophagus, CT, 71.1211

KW - Esophagus, neoplasms, 71.3131

KW - Myoma, 71.3131

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Diffuse esophageal leiomyomatosis in a patient with Alport syndrome: CT demonstration

Abstract

Keywords

ASJC Scopus subject areas

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