Curves of the achondroplastic spine: A new hypothesis

A. A. Siebens, D. S. Hungerford, N. A. Kirby

Research output: Chapter in Book/Report/Conference proceedingChapter

Abstract

The profile of the achondroplastic dwarf reflects abnormalities in the shape of the spine, particularly in the lumbosacral area. We hypothesize that these abnormalities and the resultant symptoms are secondary and avoidable rather than heritable and inevitable. Because the heads of achondroplastic children are enlarged (n = 50), loading of the vertical spine is increased. Unusually lax ligaments and misshapen vertebrae predispose the spine to yielding under vertical stress. Children and adults uniformly have hip flexion contractures (n = 105); these are hypothesized to be the result of uncorrected lumbosacral lordosis. The volume of the spinal canal, reduced by the spinal stenosis of achondroplasia, is decreased additionally by lordosis; some neurologic deficits of achondroplasia are caused by this abnormal curvature. This hypothesis bears practically on treating this common form of dwarfism.

Original languageEnglish (US)
Title of host publicationJohns Hopkins Medical Journal
Pages205-210
Number of pages6
Volume142
Edition6
StatePublished - 1978

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Spine
Achondroplasia
Lordosis
Hip Contracture
Dwarfism
Spinal Stenosis
Spinal Canal
Neurologic Manifestations
Ligaments
Head

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Siebens, A. A., Hungerford, D. S., & Kirby, N. A. (1978). Curves of the achondroplastic spine: A new hypothesis. In Johns Hopkins Medical Journal (6 ed., Vol. 142, pp. 205-210)

Curves of the achondroplastic spine : A new hypothesis. / Siebens, A. A.; Hungerford, D. S.; Kirby, N. A.

Johns Hopkins Medical Journal. Vol. 142 6. ed. 1978. p. 205-210.

Research output: Chapter in Book/Report/Conference proceedingChapter

Siebens, AA, Hungerford, DS & Kirby, NA 1978, Curves of the achondroplastic spine: A new hypothesis. in Johns Hopkins Medical Journal. 6 edn, vol. 142, pp. 205-210.
Siebens AA, Hungerford DS, Kirby NA. Curves of the achondroplastic spine: A new hypothesis. In Johns Hopkins Medical Journal. 6 ed. Vol. 142. 1978. p. 205-210
Siebens, A. A. ; Hungerford, D. S. ; Kirby, N. A. / Curves of the achondroplastic spine : A new hypothesis. Johns Hopkins Medical Journal. Vol. 142 6. ed. 1978. pp. 205-210
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