Congenital absence of the pericardium and its mimics

Research output: Contribution to journalArticle

Abstract

Congenital absence of the pericardium is a rare entity, with less than 400 cases reported in the literature. Pericardial absence is typically left sided, which results in herniation of the great vessels or portions of the heart. Patients may be asymptomatic, typical for complete defects, or can present with various degrees of chest pain in the setting of partial absence and strangulation. The finding may be isolated or associated with complex heart disease. We present a number of cases of pericardial absence that show isolated right- and left-sided defects, as well as entities in the differential diagnosis. Early recognition may decrease morbidity and mortality, resulting from delay in proper treatment.

Original languageEnglish (US)
Pages (from-to)11-17
Number of pages7
JournalJournal of Cardiovascular Computed Tomography
Volume7
Issue number1
DOIs
StatePublished - Jan 2013

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Pericardium
Chest Pain
Heart Diseases
Differential Diagnosis
Morbidity
Mortality
Therapeutics

Keywords

  • Absence
  • Congenital
  • Defect
  • Pericardial
  • Pericardium

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine
  • Radiology Nuclear Medicine and imaging

Cite this

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title = "Congenital absence of the pericardium and its mimics",
abstract = "Congenital absence of the pericardium is a rare entity, with less than 400 cases reported in the literature. Pericardial absence is typically left sided, which results in herniation of the great vessels or portions of the heart. Patients may be asymptomatic, typical for complete defects, or can present with various degrees of chest pain in the setting of partial absence and strangulation. The finding may be isolated or associated with complex heart disease. We present a number of cases of pericardial absence that show isolated right- and left-sided defects, as well as entities in the differential diagnosis. Early recognition may decrease morbidity and mortality, resulting from delay in proper treatment.",
keywords = "Absence, Congenital, Defect, Pericardial, Pericardium",
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AU - Verde, Franco

AU - Johnson, Pamela

AU - Jha, Saurabh

AU - Fishman, Elliot K

AU - Zimmerman, Stefan

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AB - Congenital absence of the pericardium is a rare entity, with less than 400 cases reported in the literature. Pericardial absence is typically left sided, which results in herniation of the great vessels or portions of the heart. Patients may be asymptomatic, typical for complete defects, or can present with various degrees of chest pain in the setting of partial absence and strangulation. The finding may be isolated or associated with complex heart disease. We present a number of cases of pericardial absence that show isolated right- and left-sided defects, as well as entities in the differential diagnosis. Early recognition may decrease morbidity and mortality, resulting from delay in proper treatment.

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