Complications after cardiovascular surgery in a case of undiagnosed spinal-bulbar muscular atrophy (Kennedy disease)

Stacey A. Skoretz, May Sann Yee, Rosemary Martino

Research output: Contribution to journalArticle

Abstract

Neurodegenerative diseases are often associated with life-threatening declines in respiratory and swallowing mechanisms. We report the case of a 70-year-old man who had postoperative dysphagia and respiratory failure that required reintubation after coronary artery bypass surgery. Impairment of the patient's speech, swallowing, and respiratory mechanisms identified during postoperative clinical and instrumental examinations was suggestive of a neurodegenerative disease. Genetic testing confirmed a diagnosis of spinal-bulbar muscular atrophy (Kennedy disease). This case report aims to highlight increased morbidity in patients with undiagnosed neuromuscular disorders in the critical care setting and the benefits of vigilant postoperative monitoring and multidisciplinary involvement throughout the care of complex patients.

Original languageEnglish (US)
JournalAmerican Journal of Critical Care
Volume21
Issue number2
StatePublished - Mar 1 2012
Externally publishedYes

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X-Linked Bulbo-Spinal Atrophy
Atrophic Muscular Disorders
Deglutition
Neurodegenerative Diseases
Genetic Testing
Critical Care
Deglutition Disorders
Coronary Artery Bypass
Respiratory Insufficiency
Patient Care
Morbidity

ASJC Scopus subject areas

  • Critical Care

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Complications after cardiovascular surgery in a case of undiagnosed spinal-bulbar muscular atrophy (Kennedy disease). / Skoretz, Stacey A.; Yee, May Sann; Martino, Rosemary.

In: American Journal of Critical Care, Vol. 21, No. 2, 01.03.2012.

Research output: Contribution to journalArticle

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