Cases of aphasia or neglect due to Creutzfeldt-Jakob disease

Argye Hillis-Trupe, Ola Selnes

Research output: Contribution to journalArticle

Abstract

Two patients with CJD whose deficits are attributable to damage to selective cognitive mechanisms are described. One patient presented with 'pure word deafness' with severe anemia and progressed to Global aphasia. EEG and SPECT showed left cortical abnormalities. The other presented with progressive left neglect and digressive speech with meager interpretive content, but never developed aphasia. EEG showed right cortical abnormalities. These cases provide evidence that CJD can begin focally and unilaterally. Several cases of progressive aphasia due to CJD have been described, but this may be the first reported case of progressive right hemisphere dysfunction due to CJD.

Original languageEnglish (US)
Pages (from-to)743-754
Number of pages12
JournalAphasiology
Volume13
Issue number9-11
DOIs
StatePublished - Sep 1999

Fingerprint

Creutzfeldt-Jakob Syndrome
Aphasia
speech disorder
neglect
Disease
Electroencephalography
deafness
Deafness
Single-Photon Emission-Computed Tomography
Anemia
deficit
damages
evidence
Neglect
Electroencephalogram
Damage
Right Hemisphere
Progressive Aphasia

ASJC Scopus subject areas

  • Clinical Neurology
  • Neurology

Cite this

Cases of aphasia or neglect due to Creutzfeldt-Jakob disease. / Hillis-Trupe, Argye; Selnes, Ola.

In: Aphasiology, Vol. 13, No. 9-11, 09.1999, p. 743-754.

Research output: Contribution to journalArticle

Hillis-Trupe, Argye ; Selnes, Ola. / Cases of aphasia or neglect due to Creutzfeldt-Jakob disease. In: Aphasiology. 1999 ; Vol. 13, No. 9-11. pp. 743-754.
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