TY - JOUR
T1 - Bilateral Duane's Retraction Syndrome
T2 - A Clinical-Pathologic Case Report
AU - Hotchkiss, Mary G.
AU - Miller, Neil R.
AU - Clark, Arthur W.
AU - Green, William R.
PY - 1980/5
Y1 - 1980/5
N2 - • Duane's retraction syndrome (DRS) is a congenital eye movement disorder characterized by abduction deficiency, adduction limitation, globe retraction, and palpebral fissure narrowing on attempted adduction. Although data from surgical and autopsy studies suggest a neurogenic cause for this disorder, only one welldocumented case of DRS has been studied pathologically, and that report was incomplete. We describe the intracranial and orbital pathology of a clinically documented case of bilateral DRS. Both abducens nuclei and nerves were absent from the brainstem, and the lateral rectus muscles were partially innervated by branches from the oculomotor nerves. This report presents evidence that a cranial nerve anomaly may cause DRS. The reason for this neurogenic abnormality is briefly discussed.
AB - • Duane's retraction syndrome (DRS) is a congenital eye movement disorder characterized by abduction deficiency, adduction limitation, globe retraction, and palpebral fissure narrowing on attempted adduction. Although data from surgical and autopsy studies suggest a neurogenic cause for this disorder, only one welldocumented case of DRS has been studied pathologically, and that report was incomplete. We describe the intracranial and orbital pathology of a clinically documented case of bilateral DRS. Both abducens nuclei and nerves were absent from the brainstem, and the lateral rectus muscles were partially innervated by branches from the oculomotor nerves. This report presents evidence that a cranial nerve anomaly may cause DRS. The reason for this neurogenic abnormality is briefly discussed.
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U2 - 10.1001/archopht.1980.01020030864013
DO - 10.1001/archopht.1980.01020030864013
M3 - Article
C2 - 7378011
AN - SCOPUS:0018893694
SN - 0003-9950
VL - 98
SP - 870
EP - 874
JO - Archives of ophthalmology
JF - Archives of ophthalmology
IS - 5
ER -