Bietti's tapetoretinal degeneration with marginal corneal dystrophy: Crystalline retinopathy

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Abstract

In 1937 Bietti reported a tapetoretinal degeneration with associated corneal deposits at the limbus. The hallmark of the disease was the crystalline characteristics of the retinal spots as well as those at the corneal limbus. Bagolini and Ioli-Spade in 1968 presented a 30 year follow-up on Bietti's cases and presented six additional cases. The present report deals with this entity in Orientals, a Chinese woman and a Japanese man. Corneal and conjunctival biopsy from the female patient revealed a lipid deposition in both fibroblasts and epithelium. The term 'crystalline retinopathy' has been added to the description of this entity since it defines the most characteristic feature of the syndrome.

Original languageEnglish (US)
Pages (from-to)164-179
Number of pages16
JournalTransactions of the American Ophthalmological Society
VolumeVol. 75
StatePublished - Jan 1 1978

ASJC Scopus subject areas

  • Ophthalmology

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