Autosomal recessive polycystic kidney disease and congenital hepatic fibrosis (ARPKD/CHF)

Baris Turkbey; Iclal Ocak; Kailash Daryanani; Esperanza Font-Montgomery; Linda Lukose; Joy Bryant; Maya Tuchman; Parvathi Mohan; Theo Heller; William A. Gahl; Peter L. Choyke; Meral Gunay-Aygun

doi:10.1007/s00247-008-1064-x

Autosomal recessive polycystic kidney disease and congenital hepatic fibrosis (ARPKD/CHF)

Baris Turkbey, Iclal Ocak, Kailash Daryanani, Esperanza Font-Montgomery, Linda Lukose, Joy Bryant, Maya Tuchman, Parvathi Mohan, Theo Heller, William A. Gahl, Peter L. Choyke, Meral Gunay-Aygun

Research output: Contribution to journal › Review article

Abstract

ARPKD/CHF is an inherited disease characterized by non-obstructive fusiform dilatation of the renal collecting ducts leading to enlarged spongiform kidneys and ductal plate malformation of the liver resulting in congenital hepatic fibrosis. ARPKD/CHF has a broad spectrum of clinical presentations involving the kidney and liver. Imaging plays an important role in the diagnosis and follow-up of ARPKD/CHF. Combined use of conventional and high-resolution US with MR cholangiography in ARPKD/CHF patients allows detailed definition of the extent of kidney and hepatobiliary manifestations without requiring ionizing radiation and contrast agents.

Original language	English (US)
Pages (from-to)	100-111
Number of pages	12
Journal	Pediatric radiology
Volume	39
Issue number	2
DOIs	https://doi.org/10.1007/s00247-008-1064-x
State	Published - Feb 1 2009
Externally published	Yes

Keywords

Autosomal recessive polycystic kidney disease
Children
Congenital hepatic fibrosis
MR cholangiography
US

ASJC Scopus subject areas

Pediatrics, Perinatology, and Child Health
Radiology Nuclear Medicine and imaging

Access to Document

10.1007/s00247-008-1064-x

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Turkbey, B., Ocak, I., Daryanani, K., Font-Montgomery, E., Lukose, L., Bryant, J., Tuchman, M., Mohan, P., Heller, T., Gahl, W. A., Choyke, P. L., & Gunay-Aygun, M. (2009). Autosomal recessive polycystic kidney disease and congenital hepatic fibrosis (ARPKD/CHF). Pediatric radiology, 39(2), 100-111. https://doi.org/10.1007/s00247-008-1064-x

Autosomal recessive polycystic kidney disease and congenital hepatic fibrosis (ARPKD/CHF). / Turkbey, Baris; Ocak, Iclal; Daryanani, Kailash; Font-Montgomery, Esperanza; Lukose, Linda; Bryant, Joy; Tuchman, Maya; Mohan, Parvathi; Heller, Theo; Gahl, William A.; Choyke, Peter L.; Gunay-Aygun, Meral.

In: Pediatric radiology, Vol. 39, No. 2, 01.02.2009, p. 100-111.

Research output: Contribution to journal › Review article

Turkbey, Baris ; Ocak, Iclal ; Daryanani, Kailash ; Font-Montgomery, Esperanza ; Lukose, Linda ; Bryant, Joy ; Tuchman, Maya ; Mohan, Parvathi ; Heller, Theo ; Gahl, William A. ; Choyke, Peter L. ; Gunay-Aygun, Meral. / Autosomal recessive polycystic kidney disease and congenital hepatic fibrosis (ARPKD/CHF). In: Pediatric radiology. 2009 ; Vol. 39, No. 2. pp. 100-111.

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