Adult cystic fibrosis

Michael P. Boyle

Research output: Contribution to journalArticlepeer-review

Abstract

Cystic fibrosis is a multisystem disease characterized primarily by chronic pulmonary infection and bronchiectasis, pancreatic exocrine impairment, and elevated sweat chloride. In the last 4 decades, new treatment strategies and aggressive nutritional management have resulted in a significant increase in expected survival, with median predicted survival in cystic fibrosis now to older than 35 years. This increase in predicted survival has also been aided by a greater appreciation of the potential variability in the presentation and severity of cystic fibrosis, resulting in identification of a growing number of mild cases. As it is estimated that within the next decade more than half of all individuals with cystic fibrosis will be aged 18 years or older, adult medicine caregivers are increasingly likely to encounter patients with cystic fibrosis and be exposed to their unique medical management.

Original languageEnglish (US)
Pages (from-to)1787-1793
Number of pages7
JournalJournal of the American Medical Association
Volume298
Issue number15
DOIs
StatePublished - Oct 17 2007

ASJC Scopus subject areas

  • Medicine(all)

Fingerprint Dive into the research topics of 'Adult cystic fibrosis'. Together they form a unique fingerprint.

Cite this