Acute Splenic Sequestration Crisis Resembling Sepsis in an Adult with Hemoglobin SC Disease

Andrea Wang-Gillam, Rita Shi Ming Lee, Eric D. Hsi, Daniel J. Brotman

Research output: Contribution to journalArticlepeer-review

7 Scopus citations

Abstract

Acute splenic sequestration crisis (ASSC) is a common complication of sickle cell anemia in children. ASSC is generally not seen in adults with the SS genotype but occasionally can be seen in adults with the SC genotype. We present a case of fulminant ASSC in an adult with hemoglobin SC who developed high fever, intense abdominal pain, leukocytosis, and jaundice.

Original languageEnglish (US)
Pages (from-to)413-415
Number of pages3
JournalSouthern medical journal
Volume97
Issue number4
DOIs
StatePublished - Apr 2004
Externally publishedYes

Keywords

  • Acute splenic sequestration crisis
  • Adults
  • Sickle cell anemia

ASJC Scopus subject areas

  • General Medicine

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