TY - JOUR
T1 - A Morgagni hernia with an absent ductus venosus
T2 - An unusual case causing unusual consequences
AU - Phillis, Maria
AU - Garcia, Alejandro V.
AU - Jelin, Eric B.
N1 - Publisher Copyright:
© 2016 The Authors
Copyright:
Copyright 2017 Elsevier B.V., All rights reserved.
PY - 2016/9/1
Y1 - 2016/9/1
N2 - A Morgagni hernia is a rare form of congenital diaphragmatic hernia (CDH), comprising only 3–5% of all CDH cases. Agenesis of the ductus venosus with direct umbilical vein blood flow to the heart is a relatively uncommon finding that is often fatal in utero. We present a case of a 2-month-old infant with Morgagni hernia and absence of the ductus venosus. These combined defects led to neovascularization of the liver, severe pulmonary hypertension and right heart failure. In this report, we describe a Morgagni hernia that's presentation resembled that of a Bochdalek hernia likely because of concomitant absence of the ductus venosus causing severe pulmonary hypertension.
AB - A Morgagni hernia is a rare form of congenital diaphragmatic hernia (CDH), comprising only 3–5% of all CDH cases. Agenesis of the ductus venosus with direct umbilical vein blood flow to the heart is a relatively uncommon finding that is often fatal in utero. We present a case of a 2-month-old infant with Morgagni hernia and absence of the ductus venosus. These combined defects led to neovascularization of the liver, severe pulmonary hypertension and right heart failure. In this report, we describe a Morgagni hernia that's presentation resembled that of a Bochdalek hernia likely because of concomitant absence of the ductus venosus causing severe pulmonary hypertension.
KW - Congenital diaphragmatic hernia
KW - Ductus venosus
KW - Liver neovascularization
KW - Morgagni hernia
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U2 - 10.1016/j.epsc.2016.06.011
DO - 10.1016/j.epsc.2016.06.011
M3 - Article
AN - SCOPUS:84979225439
SN - 2213-5766
VL - 12
SP - 16
EP - 20
JO - Journal of Pediatric Surgery Case Reports
JF - Journal of Pediatric Surgery Case Reports
ER -