A Cutaneous Marker in the Hunter Syndrome: A Report of Four Cases

Stephen D. Prystowsky, Irene H. Maumenee, Robert G. Freeman, James H. Herndon, Mary Jo Harrod

Research output: Contribution to journalArticle

Abstract

A report of four patients and review of the literature suggest that a cutaneous marker exists for the Hunter syndrome. All previously described patients with this eruption have been males with clear corneas. The distinctive lesions consist of firm ivory-white papules and nodules that may coalesce to form ridges or a reticular pattern. The papules are usually seen in symmetrical areas between the angles of the scapulas and posterior axillary lines, the pectoral regions, the nape of the neck and/or on the lateral aspects of the upper arms and thighs. These lesions are seen in both allelic forms and cannot be used to separate a benign from a rapid course.

Original languageEnglish (US)
Pages (from-to)602-605
Number of pages4
JournalArchives of Dermatology
Volume113
Issue number5
DOIs
StatePublished - 1977

Fingerprint

Mucopolysaccharidosis II
Scapula
Skin
Thigh
Cornea
Arm
Neck

ASJC Scopus subject areas

  • Dermatology

Cite this

Prystowsky, S. D., Maumenee, I. H., Freeman, R. G., Herndon, J. H., & Jo Harrod, M. (1977). A Cutaneous Marker in the Hunter Syndrome: A Report of Four Cases. Archives of Dermatology, 113(5), 602-605. https://doi.org/10.1001/archderm.1977.01640050062007

A Cutaneous Marker in the Hunter Syndrome : A Report of Four Cases. / Prystowsky, Stephen D.; Maumenee, Irene H.; Freeman, Robert G.; Herndon, James H.; Jo Harrod, Mary.

In: Archives of Dermatology, Vol. 113, No. 5, 1977, p. 602-605.

Research output: Contribution to journalArticle

Prystowsky, SD, Maumenee, IH, Freeman, RG, Herndon, JH & Jo Harrod, M 1977, 'A Cutaneous Marker in the Hunter Syndrome: A Report of Four Cases', Archives of Dermatology, vol. 113, no. 5, pp. 602-605. https://doi.org/10.1001/archderm.1977.01640050062007
Prystowsky, Stephen D. ; Maumenee, Irene H. ; Freeman, Robert G. ; Herndon, James H. ; Jo Harrod, Mary. / A Cutaneous Marker in the Hunter Syndrome : A Report of Four Cases. In: Archives of Dermatology. 1977 ; Vol. 113, No. 5. pp. 602-605.
@article{15255ddd8f2848d780dc6ad381d65c22,
title = "A Cutaneous Marker in the Hunter Syndrome: A Report of Four Cases",
abstract = "A report of four patients and review of the literature suggest that a cutaneous marker exists for the Hunter syndrome. All previously described patients with this eruption have been males with clear corneas. The distinctive lesions consist of firm ivory-white papules and nodules that may coalesce to form ridges or a reticular pattern. The papules are usually seen in symmetrical areas between the angles of the scapulas and posterior axillary lines, the pectoral regions, the nape of the neck and/or on the lateral aspects of the upper arms and thighs. These lesions are seen in both allelic forms and cannot be used to separate a benign from a rapid course.",
author = "Prystowsky, {Stephen D.} and Maumenee, {Irene H.} and Freeman, {Robert G.} and Herndon, {James H.} and {Jo Harrod}, Mary",
year = "1977",
doi = "10.1001/archderm.1977.01640050062007",
language = "English (US)",
volume = "113",
pages = "602--605",
journal = "JAMA Dermatology",
issn = "2168-6068",
publisher = "American Medical Association",
number = "5",

}

TY - JOUR

T1 - A Cutaneous Marker in the Hunter Syndrome

T2 - A Report of Four Cases

AU - Prystowsky, Stephen D.

AU - Maumenee, Irene H.

AU - Freeman, Robert G.

AU - Herndon, James H.

AU - Jo Harrod, Mary

PY - 1977

Y1 - 1977

N2 - A report of four patients and review of the literature suggest that a cutaneous marker exists for the Hunter syndrome. All previously described patients with this eruption have been males with clear corneas. The distinctive lesions consist of firm ivory-white papules and nodules that may coalesce to form ridges or a reticular pattern. The papules are usually seen in symmetrical areas between the angles of the scapulas and posterior axillary lines, the pectoral regions, the nape of the neck and/or on the lateral aspects of the upper arms and thighs. These lesions are seen in both allelic forms and cannot be used to separate a benign from a rapid course.

AB - A report of four patients and review of the literature suggest that a cutaneous marker exists for the Hunter syndrome. All previously described patients with this eruption have been males with clear corneas. The distinctive lesions consist of firm ivory-white papules and nodules that may coalesce to form ridges or a reticular pattern. The papules are usually seen in symmetrical areas between the angles of the scapulas and posterior axillary lines, the pectoral regions, the nape of the neck and/or on the lateral aspects of the upper arms and thighs. These lesions are seen in both allelic forms and cannot be used to separate a benign from a rapid course.

UR - http://www.scopus.com/inward/record.url?scp=84948007372&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=84948007372&partnerID=8YFLogxK

U2 - 10.1001/archderm.1977.01640050062007

DO - 10.1001/archderm.1977.01640050062007

M3 - Article

AN - SCOPUS:84948007372

VL - 113

SP - 602

EP - 605

JO - JAMA Dermatology

JF - JAMA Dermatology

SN - 2168-6068

IS - 5

ER -